Atresia of pulmonary artery digital illustration

Atresia of pulmonary artery Save


ICD-10 code: Q25.5

Chapter: Congenital malformations, deformations and chromosomal abnormalities

Understanding Atresia of Pulmonary Artery

Atresia of the pulmonary artery is a rare congenital heart condition that affects infants and children. It is characterized by the complete blockage or absence of the pulmonary artery, which is responsible for carrying oxygen-poor blood from the heart to the lungs. This results in a lack of oxygen in the bloodstream leading to complications such as cyanosis, respiratory distress, and heart failure.

  1. Causes: Atresia of the pulmonary artery is caused by a defect in the development of the heart during fetal growth. It can occur alone or in combination with other heart defects such as ventricular septal defect (VSD) or atrial septal defect (ASD).
  2. Symptoms: Symptoms of atresia of the pulmonary artery depend on the severity of the condition. Infants with severe atresia may experience cyanosis, rapid breathing, poor feeding, and failure to thrive. Children with mild atresia may have no symptoms or only mild shortness of breath during physical activity.
  3. Diagnosis: The diagnosis of atresia of the pulmonary artery is usually made during fetal ultrasound or shortly after birth. Additional tests such as echocardiogram, cardiac catheterization, and MRI may be needed to determine the severity of the condition and plan treatment.
  4. Treatment: Treatment for atresia of the pulmonary artery usually involves surgery. The goal of surgery is to create a new pathway for blood flow to the lungs. This can be done through a procedure called a Blalock-Taussig shunt or a complete repair of the pulmonary artery. Medications may also be prescribed to manage symptoms and improve heart function.
  5. Prognosis: The prognosis for infants with atresia of the pulmonary artery depends on the severity of the condition and the success of treatment. With prompt diagnosis and appropriate treatment, many infants with atresia can live relatively normal lives. However, some may require ongoing medical care and monitoring throughout their lives.

In conclusion, atresia of the pulmonary artery is a rare but serious heart condition that requires prompt diagnosis and treatment. If you suspect that your child may have this condition, it is important to seek medical attention right away. With proper treatment, many children with atresia can live healthy and fulfilling lives.

Diagnosis Codes for Atresia of pulmonary artery | Q25.5