Default disease illustration

Other forms of systemic sclerosis Save


ICD-10 code: M34.8

Chapter: Diseases of the musculoskeletal system and connective tissue

Other Forms of Systemic Sclerosis

Systemic sclerosis, also known as scleroderma, is a rare autoimmune disease that causes hardening and thickening of the skin and connective tissues. While the most common form of systemic sclerosis affects the skin and internal organs, there are other forms of the disease that can affect specific parts of the body.

  1. Localized scleroderma: This type of scleroderma only affects the skin and does not involve internal organs. It is also known as morphea and can appear as patches or plaques of hard, thick skin.
  2. Scleroderma sine scleroderma: This form of the disease affects internal organs without causing skin thickening or hardening. Symptoms may include shortness of breath, difficulty swallowing, and gastrointestinal issues.
  3. Systemic sclerosis overlap syndrome: This is when a person has symptoms of systemic sclerosis as well as another autoimmune disease. Examples include mixed connective tissue disease and systemic lupus erythematosus.

Diagnosis of these other forms of systemic sclerosis can be challenging, as symptoms may not be as visible as in the most common form of the disease. Treatment options may vary depending on the specific form of the disease and the organs affected.

It is important for individuals with systemic sclerosis to work closely with their healthcare team to monitor symptoms and manage the disease. This may include medications, physical therapy, and other supportive measures.

While systemic sclerosis can be a challenging and complex disease, understanding the different forms of the disease can help individuals and their loved ones better navigate its impact on their lives.