Other interstitial  lung diseases of childhood digital illustration

Other interstitial lung diseases of childhood Save


ICD-10 code: J84.84

Chapter: Diseases of the respiratory system

Other interstitial lung diseases of childhood

Interstitial lung diseases refer to a group of disorders that affect the lung tissue or the space between the air sacs of the lungs. While some interstitial lung diseases are well-known, such as idiopathic pulmonary fibrosis or sarcoidosis, there are other types of interstitial lung diseases that are less familiar but can still have a significant impact on children's health.

  1. Surfactant protein deficiencies: Surfactant proteins are essential for keeping the air sacs in the lungs open, allowing air to flow in and out. When there is a deficiency in these proteins, it can lead to respiratory distress syndrome (RDS) in newborns or interstitial lung disease in older children.
  2. Lymphocytic interstitial pneumonitis (LIP): LIP is a rare disorder characterized by inflammation and damage to the lung tissue, leading to coughing, shortness of breath, and fatigue. It is more common in children with underlying autoimmune disorders or immune deficiencies.
  3. Alveolar proteinosis: In this disorder, a buildup of protein material in the air sacs of the lungs can interfere with breathing and lead to coughing, fatigue, and weight loss. While it is rare in children, it can be caused by genetic mutations or exposure to environmental toxins.
  4. Histiocytosis: Histiocytosis is a group of disorders in which histiocytes, a type of immune cell, build up in various tissues in the body, including the lungs. Depending on the severity and location of the histiocytosis, it can cause interstitial lung disease and other respiratory symptoms.

Diagnosing and managing interstitial lung diseases in children can be challenging, as symptoms can be nonspecific and may overlap with other respiratory conditions. If your child is experiencing persistent coughing, shortness of breath, or other respiratory symptoms, it is important to seek medical attention and work with a healthcare provider to determine the underlying cause and develop an appropriate treatment plan.