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Other interstitial pulmonary diseases with fibrosis Save


ICD-10 code: J84.1

Chapter: Diseases of the respiratory system

Other interstitial pulmonary diseases with fibrosis

Fibrosis is a condition in which the lung tissues become scarred, leading to breathing difficulties and reduced lung function. While idiopathic pulmonary fibrosis (IPF) is the most common form of interstitial pulmonary disease with fibrosis, there are several other types that can affect the lungs. Here are some of the other interstitial pulmonary diseases with fibrosis:

  1. Connective tissue disease-associated interstitial lung disease (CTD-ILD)
  2. CTD-ILD refers to a group of conditions that involve both connective tissue disorders and interstitial lung diseases. Examples of these conditions include rheumatoid arthritis, lupus, and scleroderma. Patients with CTD-ILD often experience symptoms such as shortness of breath, coughing, and chest pain. Treatment typically involves managing the underlying connective tissue disease, along with medications to reduce inflammation and fibrosis in the lungs.

  3. Hypersensitivity pneumonitis (HP)
  4. HP is a type of interstitial lung disease that occurs when the lungs become inflamed due to exposure to certain environmental triggers, such as mold, bird droppings, or chemicals. Symptoms of HP can include coughing, fever, and shortness of breath. Treatment involves identifying and avoiding the triggers that cause the condition, along with medications to reduce inflammation and fibrosis in the lungs.

  5. Sarcoidosis
  6. Sarcoidosis is a condition in which small clusters of cells (granulomas) form in various parts of the body, including the lungs. When sarcoidosis affects the lungs, it can lead to interstitial lung disease with fibrosis. Symptoms of sarcoidosis can include shortness of breath, coughing, and chest pain. Treatment typically involves medications to reduce inflammation and fibrosis in the lungs.

  7. Drug-induced interstitial lung disease (DI-ILD)
  8. DI-ILD is a type of lung disease that occurs as a side effect of certain medications. Symptoms of DI-ILD can include coughing, shortness of breath, and fever. Treatment typically involves discontinuing the medication that caused the condition, along with medications to reduce inflammation and fibrosis in the lungs.

If you are experiencing symptoms of interstitial lung disease with fibrosis, it is important to see a healthcare provider for diagnosis and treatment. While IPF is the most common form of this condition, there are several other types that can affect the lungs. With proper management and treatment, many patients with interstitial lung disease with fibrosis can experience improved lung function and quality of life.

Diagnosis Codes for Other interstitial pulmonary diseases with fibrosis | J84.1