Other necrotizing vasculopathies digital illustration

Other necrotizing vasculopathies Save


ICD-10 code: M31

Chapter: Diseases of the musculoskeletal system and connective tissue

What Are Other Necrotizing Vasculopathies?

Necrotizing vasculopathies are a group of rare disorders that affect the blood vessels, leading to inflammation and damage to the vessel walls. Some of the more well-known types of necrotizing vasculopathies include polyarteritis nodosa and granulomatosis with polyangiitis. However, there are other types of necrotizing vasculopathies that are less commonly known but still important to be aware of.

  1. Thromboangiitis obliterans - Also known as Buerger's disease, thromboangiitis obliterans is a type of necrotizing vasculopathy that affects the small and medium-sized arteries and veins in the arms and legs. It is most commonly seen in young men who smoke, and can lead to tissue death (gangrene) if left untreated.
  2. Behçet's disease - Behçet's disease is a type of autoimmune disorder that can cause inflammation and damage to blood vessels throughout the body, including the arteries and veins. It can lead to a variety of symptoms, including mouth and genital ulcers, skin rashes, and eye inflammation. In severe cases, it can cause blindness.
  3. Takayasu arteritis - Takayasu arteritis is a type of vasculitis that affects the large arteries, particularly those in the chest and abdomen. It can cause a variety of symptoms, including chest pain, fatigue, and muscle aches. If left untreated, it can lead to damage to the heart, kidneys, and other organs.
  4. Giant cell arteritis - Giant cell arteritis is a type of vasculitis that affects the medium and large arteries, particularly those in the head and neck. It can cause a variety of symptoms, including headaches, jaw pain, and vision problems. If left untreated, it can lead to blindness or stroke.

Other rare types of necrotizing vasculopathies include Kawasaki disease, cutaneous small-vessel vasculitis, and microscopic polyangiitis. While these disorders are rare, it's important to be aware of them in case you or a loved one experiences symptoms that could be related to a vasculopathy.

If you suspect that you may have a necrotizing vasculopathy, it's important to seek medical attention right away. Your doctor can perform tests to diagnose the condition and recommend appropriate treatment.