Supravalvular aortic stenosis Save
ICD-10 code: Q25.3
Chapter: Congenital malformations, deformations and chromosomal abnormalities
Supravalvular Aortic Stenosis: What You Need to Know
Supravalvular aortic stenosis (SVAS) is a rare heart condition that affects the aortic valve and the main artery that carries blood from the heart to the body. This condition occurs when there is a narrowing in the aorta, which can obstruct blood flow and cause serious health problems.
SVAS can be a congenital condition, meaning that it is present at birth, or it can develop later in life as a result of other medical conditions or procedures. Symptoms of SVAS may include shortness of breath, chest pain, fatigue, and fainting. However, some people with this condition may not experience any symptoms at all.
Causes of Supravalvular Aortic Stenosis
The exact cause of SVAS is not fully understood, but it is believed to be related to a genetic mutation that affects the formation and function of the aortic valve and the aorta. In some cases, SVAS may also be caused by other medical conditions, such as Williams syndrome or other connective tissue disorders.
Treatment Options for Supravalvular Aortic Stenosis
Treatment for SVAS will depend on the severity of the condition and the individual needs of the patient. In mild cases, treatment may not be necessary, and the condition may be monitored with regular check-ups and tests. However, in more severe cases, treatment options may include medications, surgery, or other medical procedures to improve blood flow and reduce the risk of complications.
- Medications: Certain medications may be prescribed to help manage symptoms of SVAS, such as high blood pressure or chest pain.
- Surgery: In some cases, surgery may be necessary to repair or replace the aortic valve and/or widen the narrowed aorta.
- Balloon angioplasty: This procedure involves inserting a small catheter with a balloon on the end into the narrowed area of the aorta and inflating the balloon to widen the artery.
Living with Supravalvular Aortic Stenosis
If you or a loved one has been diagnosed with SVAS, it is important to work closely with your healthcare provider to develop a treatment plan that meets your individual needs. In addition, it is important to maintain a healthy lifestyle by eating a nutritious diet, getting regular exercise, and avoiding smoking and other harmful habits.
With proper treatment and management, many people with SVAS are able to live healthy and fulfilling lives. However, it is important to be aware of the potential risks and complications associated with this condition and to take steps to reduce your risk of developing serious health problems.