Vogt-Koyanagi syndrome digital illustration

Vogt-Koyanagi syndrome Save

ICD-10 code: H20.82

Chapter: Diseases of the eye and adnexia

Vogt-Koyanagi Syndrome: Causes, Symptoms, and Treatment

Vogt-Koyanagi Syndrome (VKS), also known as Uveomeningoencephalitis, is a rare autoimmune disorder that affects various organs of the body. It is characterized by inflammation in the eyes, ears, skin, and the lining of the brain and spinal cord. VKS is more common in people with Asian, Native American, and Hispanic ethnicity. Here are some of the causes, symptoms, and treatments of VKS.

Causes of VKS

The exact cause of VKS is unknown. However, it is believed to be an autoimmune disorder, where the body's immune system mistakenly attacks its own cells and tissues. Some of the risk factors that increase the chances of developing VKS include family history of VKS, viral infections, and exposure to chemicals or toxins.

Symptoms of VKS
  1. Eye-related symptoms: The initial symptoms of VKS usually start with inflammation in the eyes, which can lead to vision problems, eye pain, sensitivity to light, and redness.
  2. Ear-related symptoms: VKS can also cause inflammation in the ears, leading to hearing loss, ringing in the ears, and dizziness.
  3. Skin-related symptoms: VKS can cause skin changes, such as vitiligo, which is a loss of skin pigmentation, and poliosis, which is a loss of hair pigmentation.
  4. Neurological symptoms: VKS can cause inflammation in the lining of the brain and spinal cord, leading to headaches, meningitis, and other neurological problems.
Treatment of VKS

There is no cure for VKS, but early diagnosis and treatment can help manage the symptoms and prevent complications. Treatment usually involves the use of corticosteroids and other immunosuppressive drugs to reduce inflammation and suppress the immune system. Other treatments may include eye drops, surgery, and physical therapy.

If you experience any of the symptoms of VKS, it is important to seek medical attention immediately. Your doctor may refer you to a specialist, such as an ophthalmologist or neurologist, for further evaluation and treatment. With proper treatment and management, most people with VKS can lead a normal life.