Double aortic arch digital illustration

Double aortic arch Save


ICD-10 code: Q25.45

Disease category: Q25.4: Other congenital malformations of aorta

Understanding Double Aortic Arch

Double aortic arch, also known as vascular ring anomaly, is a congenital heart defect that occurs during fetal development. It is a rare condition where the aorta, the main artery that carries oxygenated blood from the heart to the rest of the body, forms an abnormal shape.

This condition is caused by an error in the development of the aortic arches, which are the embryonic blood vessels that form the aorta. Normally, during development, the aortic arches fuse together to form a single arch. However, in double aortic arch, the arches do not fuse completely, resulting in two separate arches on either side of the trachea, or windpipe.

Double aortic arch can cause compression of the trachea and esophagus, leading to respiratory and feeding difficulties in infants. Symptoms may include noisy breathing, wheezing, coughing, difficulty swallowing, and poor weight gain. However, the severity of symptoms can vary from person to person.

  1. Diagnosis: Double aortic arch is typically diagnosed in infancy or early childhood. Diagnostic tests such as X-rays, echocardiography, and computed tomography (CT) scans can help identify the abnormality and determine its severity.
  2. Symptom management: Treatment for double aortic arch focuses on relieving the symptoms caused by compression of the trachea and esophagus. This may involve medications to reduce inflammation, breathing treatments, and dietary modifications to aid in swallowing.
  3. Prognosis: With proper symptom management, most individuals with double aortic arch can lead normal lives. However, regular follow-up with a healthcare provider is essential to monitor the condition and ensure adequate growth and development.
  4. Complications: In some cases, complications such as recurrent respiratory infections or difficulty gaining weight may occur. These may require additional medical interventions to address the specific issues.

In conclusion, double aortic arch is a rare congenital heart defect where the aorta forms an abnormal shape due to an error in development. While it can cause respiratory and feeding difficulties, proper symptom management can help individuals live normal lives. If you suspect your child may have double aortic arch, seeking medical evaluation and guidance is crucial for appropriate diagnosis and treatment.

Treatment of Double aortic arch:

Treatment Options for Double Aortic Arch

Double aortic arch (DAA) is a rare congenital heart defect where the aorta, the main artery that carries oxygen-rich blood from the heart to the body, is split into two separate vessels. This condition can cause compression of the trachea and esophagus, leading to respiratory and feeding difficulties. Early detection and timely treatment are...

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