Endothelial corneal dystrophy digital illustration

Endothelial corneal dystrophy Save


ICD-10 code: H18.51

Disease category: H18.5: Hereditary corneal dystrophies

Understanding Endothelial Corneal Dystrophy

Endothelial corneal dystrophy is a rare and progressive eye condition that affects the endothelial cells of the cornea. The cornea is the clear, dome-shaped surface at the front of the eye that plays a crucial role in focusing light onto the retina. When the endothelial cells are damaged or dysfunctional, it can lead to impaired vision and other complications.

There are three main types of endothelial corneal dystrophy: Fuchs' endothelial dystrophy, posterior polymorphous corneal dystrophy, and congenital hereditary endothelial dystrophy. Each type has distinct characteristics and may present with different symptoms.

  1. Fuchs' endothelial dystrophy: This is the most common form of endothelial corneal dystrophy. It typically affects individuals over the age of 40 and progresses slowly over time. Symptoms may include blurred or hazy vision, sensitivity to light, and glare.
  2. Posterior polymorphous corneal dystrophy: This type usually manifests during childhood or early adulthood. It is characterized by the abnormal growth of endothelial cells, leading to corneal clouding, blisters, and vision problems.
  3. Congenital hereditary endothelial dystrophy: This rare condition is present at birth and often affects both eyes. Infants with this form of dystrophy may have cloudy corneas, poor vision, and abnormal iris development.

Although the exact causes of endothelial corneal dystrophy are not fully understood, genetic factors are believed to play a significant role. The condition can be inherited within families or occur sporadically without a family history.

Diagnosis of endothelial corneal dystrophy involves a comprehensive eye examination, including visual acuity tests, corneal thickness measurements, and evaluation of the endothelial cell count. Treatment options for this condition primarily focus on managing symptoms and preventing complications, but it's important to consult with an ophthalmologist for a personalized treatment plan.

Overall, endothelial corneal dystrophy is a complex eye condition that requires proper diagnosis and management. If you suspect any symptoms or have concerns about your eye health, it is advisable to seek professional medical advice.

Treatment of Endothelial corneal dystrophy:

Understanding Endothelial Corneal Dystrophy and Its Treatment Options

Endothelial corneal dystrophy is a rare eye condition that affects the innermost layer of the cornea. This condition hampers the normal functioning of the corneal endothelium, leading to vision problems such as blurred vision, glare, and distortion. If you or someone you know has been diagnosed with endothelial c...

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