Persistent left superior vena cava digital illustration

Persistent left superior vena cava Save


ICD-10 code: Q26.1

Disease category: Q26: Congenital malformations of great veins

Persistent Left Superior Vena Cava: An Overview

Persistent left superior vena cava (PLSVC) is a rare congenital anomaly of the cardiovascular system. In normal circumstances, the superior vena cava carries deoxygenated blood from the upper body to the right atrium of the heart. However, in individuals with PLSVC, a small portion of the superior vena cava fails to regress during fetal development, resulting in a persistent connection to the left atrium.

This condition occurs in approximately 0.3-0.5% of the general population, making it a relatively uncommon anomaly. PLSVC is often discovered incidentally during medical tests or procedures, as it rarely causes symptoms or health issues. Nevertheless, understanding this anomaly is essential for accurate medical diagnoses and treatment planning.

Causes and Diagnosis

The exact cause of PLSVC is unknown, but it is believed to occur during early embryonic development when the venous system is forming. It is thought to be an inherited condition, as it is often seen in families with a history of congenital heart defects. However, PLSVC can also occur sporadically without any apparent genetic link.

Diagnosing PLSVC typically involves imaging tests such as echocardiography, magnetic resonance imaging (MRI), or computed tomography (CT) scans. These tests allow healthcare professionals to visualize the heart and blood vessels, detecting any abnormalities in the venous system.

Implications and Associated Conditions

Most individuals with PLSVC lead normal lives without any complications. However, PLSVC can sometimes be associated with other cardiac abnormalities, such as atrial septal defects (ASDs), ventricular septal defects (VSDs), or abnormalities in the electrical conduction system of the heart.

In some cases, PLSVC can pose challenges during medical procedures, particularly when accessing the right side of the heart through the superior vena cava. Healthcare professionals must be aware of this anatomical variation to minimize any potential risks during interventions.

Treatment Options

While treatment for PLSVC is not typically necessary, it is important for individuals with this condition to inform their healthcare providers. This information ensures that any future medical interventions or procedures can be performed safely and effectively.

  1. Regular follow-up appointments with a cardiologist are often recommended to monitor the condition and assess for any associated abnormalities.
  2. In certain cases, if PLSVC is accompanied by other significant heart defects, surgical intervention may be necessary. However, treatment decisions are based on individual circumstances and determined by a team of healthcare professionals.

In conclusion, persistent left superior vena cava is a rare congenital anomaly of the cardiovascular system that

Treatment of Persistent left superior vena cava:

Treatment Options for Persistent Left Superior Vena Cava

Persistent left superior vena cava (PLSVC) is a rare congenital abnormality where the major vein responsible for carrying deoxygenated blood from the upper body to the heart is not connected to the right atrium as it should be. Instead, it connects to the left atrium.

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