Pseudosarcomatous fibromatosis Save

Pseudosarcomatous Fibromatosis: A Rare Benign Soft Tissue Tumor

Pseudosarcomatous fibromatosis, also known as nodular fasciitis or infiltrative fasciitis, is a rare benign soft tissue tumor that predominantly affects young adults. It is characterized by rapid growth, a fibroblastic proliferation pattern, and a tendency to mimic malignant sarcomas. Although the exact cause of pseudosarcomatous fibromatosis is unknown, it is believed to be a reactive process triggered by trauma or injury.

Unlike true sarcomas, pseudosarcomatous fibromatosis does not metastasize or invade nearby tissues. It commonly presents as a solitary, painless, rapidly growing mass, most commonly found in the subcutaneous tissues of the upper extremities, trunk, or head and neck region. The tumor is typically firm, well-circumscribed, and may be mistaken for a sarcoma upon initial examination.

Signs and Symptoms:

1. Rapidly growing mass
2. Painless lump
3. Located in subcutaneous tissues
4. Commonly found in upper extremities, trunk, or head and neck region

Diagnosis:

Diagnosing pseudosarcomatous fibromatosis requires a careful evaluation of the patient's medical history, physical examination, and imaging studies. In some cases, a biopsy may be necessary to confirm the diagnosis. Microscopically, the tumor exhibits a characteristic storiform or whirling pattern of spindle cells, with scattered inflammatory cells and myofibroblasts.

Treatment:

The primary treatment for pseudosarcomatous fibromatosis involves surgical excision of the tumor. Complete resection is curative, and recurrence is rare. However, due to the aggressive growth nature of the tumor, close follow-up is recommended to monitor for any signs of recurrence or residual disease.

In conclusion, pseudosarcomatous fibromatosis is a rare benign soft tissue tumor that mimics malignant sarcomas. Though it can be alarming, it is important to note that this tumor does not metastasize or invade surrounding tissues. Prompt diagnosis and appropriate management through surgical excision can effectively treat this condition.