Sickle-cell thalassemia beta zero with crisis with other specified complication digital illustration

Sickle-cell thalassemia beta zero with crisis with other specified complication Save


ICD-10 code: D57.438

Disease category: None

Sickle-Cell Thalassemia Beta Zero with Crisis and Other Specified Complications

Sickle-cell thalassemia beta zero with crisis and other specified complications is a rare genetic disorder that affects the production of hemoglobin in the body. Hemoglobin is a protein in red blood cells that carries oxygen to all parts of the body. In people with sickle-cell thalassemia beta zero, the body produces an abnormal form of hemoglobin that can cause red blood cells to become stiff and misshapen.

When red blood cells become misshapen, they can get stuck in small blood vessels, blocking blood flow and causing a painful condition called a sickle-cell crisis. Sickle-cell crises can occur anywhere in the body, but most commonly affect the bones, joints, and organs.

In addition to sickle-cell crises, people with sickle-cell thalassemia beta zero may also experience other complications, such as:

  1. Stroke: When blood flow to the brain is blocked by sickle cells, it can cause a stroke.
  2. Infections: People with sickle-cell thalassemia beta zero are at increased risk of infections, particularly from bacteria that can cause pneumonia, meningitis, and sepsis.
  3. Acute Chest Syndrome: A condition that occurs when sickle cells block blood vessels in the lungs, causing chest pain, difficulty breathing, and a high fever.
  4. Priapism: A painful condition in which the penis becomes erect and stays that way for an extended period of time, potentially causing damage to the penis.

Diagnosis of sickle-cell thalassemia beta zero with crisis and other specified complications is typically made through a blood test that measures the level of abnormal hemoglobin in the body. Treatment for sickle-cell thalassemia beta zero with crisis and other specified complications is focused on managing symptoms and preventing complications. This may include medications to manage pain, antibiotics to prevent infections, and blood transfusions to increase the number of healthy red blood cells in the body.

Living with sickle-cell thalassemia beta zero with crisis and other specified complications can be challenging, but with proper management and care, people with this condition can lead full and productive lives.

Treatment of Sickle-cell thalassemia beta zero with crisis with other specified complication:

Sickle-cell thalassemia beta zero with crisis with other specified complications refers to a severe form of sickle cell disease that affects the production of hemoglobin in the body. Hemoglobin is a protein found in red blood cells that carries oxygen from the lungs to the rest of the body. In sickle cell disease, the production of normal hemoglobin is disrupted, leading to the formation of abn...

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