Total anomalous pulmonary venous connection digital illustration

Total anomalous pulmonary venous connection Save


ICD-10 code: Q26.2

Disease category: Q26: Congenital malformations of great veins

Total Anomalous Pulmonary Venous Connection: Understanding the Condition

Total anomalous pulmonary venous connection (TAPVC) is a rare congenital heart defect that affects newborns. In this condition, the pulmonary veins, which normally carry oxygen-rich blood from the lungs to the heart, are improperly connected to the heart. Instead of connecting to the left atrium, the pulmonary veins attach to other blood vessels or even the right atrium, resulting in abnormal blood flow.

TAPVC can be categorized into four types based on the location of the anomalous connection. These types include supracardiac, cardiac, infracardiac, and mixed, each presenting unique challenges and symptoms. However, regardless of the type, TAPVC leads to insufficient oxygen supply to the body, causing various complications.

  1. Symptoms: Common symptoms of TAPVC include rapid breathing, poor feeding, cyanosis (a bluish tint to the skin), fatigue, and frequent respiratory infections. The severity of symptoms depends on the type of TAPVC and the extent of the abnormal connection.
  2. Diagnosis: TAPVC is usually diagnosed shortly after birth or during infancy. Doctors may suspect TAPVC based on the symptoms and may confirm the diagnosis through various tests, such as echocardiography, chest X-rays, or cardiac catheterization.
  3. Causes: The exact cause of TAPVC is unknown. However, it is believed to result from abnormal development during the early stages of fetal growth. Genetic factors may also play a role in increasing the risk of TAPVC.
  4. Treatment: (Please note that treatment information is not provided in this article.)

Early detection and prompt medical intervention are crucial for managing TAPVC. Treatment typically involves surgical correction to reroute the abnormal pulmonary veins and restore normal blood flow. Different surgical techniques can be employed based on the specific type and severity of TAPVC. However, the success of treatment largely depends on the individual case and the overall health of the patient.

In conclusion, total anomalous pulmonary venous connection is a rare congenital heart defect that affects how the pulmonary veins connect to the heart. Understanding the symptoms, diagnosis, and causes of TAPVC is essential for early detection and appropriate medical intervention. If you suspect your child may have TAPVC, it is important to consult a healthcare professional for a comprehensive evaluation and further guidance.

Treatment of Total anomalous pulmonary venous connection:

Treatment Options for Total Anomalous Pulmonary Venous Connection

Total anomalous pulmonary venous connection (TAPVC) is a rare congenital heart defect where the pulmonary veins, responsible for carrying oxygen-rich blood from the lungs to the heart, connect abnormally to the right atrium or other nearby blood vessels. This condition requires immediate medical attention and treatme...

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