Other specified types of T/NK-cell lymphoma digital illustration

Other specified types of T/NK-cell lymphoma Save


ICD-10 code: C86

Chapter: Neoplasms

Understanding Other specified types of T/NK-cell lymphoma

T-cell and natural killer (NK) cell lymphomas are a group of rare and aggressive cancers that affect the immune system. Other specified types of T/NK-cell lymphoma represent a subset of these types of cancers that do not fit into any other category of T-cell or NK-cell lymphoma.

Other specified types of T/NK-cell lymphoma are characterized by the presence of abnormal T-cells or NK cells that grow uncontrollably, leading to the formation of tumors in various parts of the body, including the skin, lymph nodes, and organs such as the liver, spleen, and bone marrow.

There are several subtypes of other specified types of T/NK-cell lymphoma, including adult T-cell leukemia/lymphoma (ATL), primary cutaneous gamma-delta T-cell lymphoma, and primary cutaneous CD30-positive T-cell lymphoproliferative disorders.

ATL is a rare and aggressive form of T-cell lymphoma that is caused by human T-cell leukemia virus type 1 (HTLV-1). This virus is endemic in certain regions of the world, including Japan, the Caribbean, and parts of Central and South America. ATL can present as either an aggressive acute form or a chronic form that progresses slowly over time.

Primary cutaneous gamma-delta T-cell lymphoma is a rare subtype of T-cell lymphoma that primarily affects the skin. It is characterized by the presence of abnormal T-cells that express the gamma-delta T-cell receptor. This subtype of T-cell lymphoma is typically slow-growing and has a good prognosis with appropriate treatment.

Primary cutaneous CD30-positive T-cell lymphoproliferative disorders are a group of rare T-cell lymphomas that are characterized by the overexpression of the CD30 protein on the surface of abnormal T-cells. These lymphomas primarily affect the skin and have a good prognosis with appropriate treatment.

  1. ATL is caused by human T-cell leukemia virus type 1 (HTLV-1).
  2. Primary cutaneous gamma-delta T-cell lymphoma is characterized by the presence of abnormal T-cells that express the gamma-delta T-cell receptor.
  3. Primary cutaneous CD30-positive T-cell lymphoproliferative disorders are characterized by the overexpression of the CD30 protein on the surface of abnormal T-cells.

Other specified types of T/NK-cell lymphoma are rare and aggressive cancers that require prompt diagnosis and appropriate treatment. Treatment options may include chemotherapy, radiation therapy, immunotherapy, and stem cell transplantation.

If you suspect that you or a loved one may have other specified types of T/NK-cell lymphoma, it is important to seek medical attention promptly. Your